Urological conservative management of a patient with tuberous sclerosis complex (Bourneville disease).

نویسندگان

  • Jorge Sague Larrea
  • Luis Borrego Pino
  • Rene Salas Cabrera
  • Ariel Laurencio Mena
چکیده

OBJECTIVE To report the clinical and radiological data of a 23-year-woman with bilateral angiomyolipoma and Tuberous Sclerosis with conservative treatment. METHODS The patient underwent conservative urological management, based on clinical and complementary tests data (ultrasonography, CT scanning, excretory urogram, and laboratory). Monitoring was carried out in external consultation by the urooncology group. In some occasions she was hospitalized due to distant geographical factors. RESULTS This patient provides long-term outcome of AML with Tuberous Sclerosis followed by repeated evaluation to define the conservative management or not. Ultrasound and CT scan were two basic studies to maintain conservative treatment, as well as a good clinical evaluation. CONCLUSIONS Renal lesions associated with tuberous sclerosis are frequent and serious. Monitoring should be based on a careful monitoring since the renal lesions are the second death cause after the lesions of the nervous system. This case report provides long-term outcome of AML with tuberous sclerosis, that can be followed expectantly with repeated evaluations to define the clinical significance.

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عنوان ژورنال:
  • Archivos espanoles de urologia

دوره 62 7  شماره 

صفحات  -

تاریخ انتشار 2009